½Å¿ì Á¾±« Çü¼º°ú ÃéÀå ħ¹üÀ» µ¿¹ÝÇÑ IgG4 ¿¬°ü °æÈ¼º Áúȯ 1¿¹
A Case of IgG4-Related Pancreas and Kidney Disease Mimicking a Renal Pelvic Malignancy
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±è¿ìÀç(Kim Woo-Jae) - µ¿¾Æ´ëÇб³ Àǰú´ëÇÐ ³»°úÇб³½Ç
³ë¸íȯ(Roh Myung-Hwan) - µ¿¾Æ´ëÇб³ Àǰú´ëÇÐ ³»°úÇб³½Ç
·ùÃæÇå(Ryu Choong-Heon) - µ¿¾Æ´ëÇб³ Àǰú´ëÇÐ ³»°úÇб³½Ç
ÇѽÂÈñ(Han Seung-Hee) - µ¿¾Æ´ëÇб³ Àǰú´ëÇÐ ³»°úÇб³½Ç
³²È¼º(Nam Hwa-Seong) - µ¿¾Æ´ëÇб³ Àǰú´ëÇÐ ³»°úÇб³½Ç
ÇÑÁöÀº(Han Ji-Eun) - µ¿¾Æ´ëÇб³ Àǰú´ëÇÐ ³»°úÇб³½Ç
È«¼÷Èñ(Hong Sook-Hee) - µ¿¾Æ´ëÇб³ Àǰú´ëÇÐ º´¸®Çб³½Ç
Abstract
IgG4-related sclerosing disease is a disease entity that has recently attracted attention, manifesting as a multiorgan disease characterized by high serum IgG4 levels, extensive IgG4-positive plasma cells and lymphocyte infiltration of the affected organs, with the pancreas (autoimmune pancreatitis) and kidney as representative targets. In cases of renal involvement, parenchymal lesions are predominant, such as renal cortical lesions or diffuse renal enlargement. However, mass-like lesions involving the renal pelvis are very rare, and mass forming or pelvic involvement types should be distinguished from lymphomas, metastatic cancers and other genitourinary malignancies to avoid unnecessary surgery. Herein, we report a case of IgG4-related sclerosing disease involving the kidney as an unusual involvement pattern presenting as a mass-like lesion with pelvic and perirenal involvement.
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¸é¿ª±Û·ÎºÒ¸° G4 ¿¬°ü¼º ½ÅÀå Áúȯ, ÀÚ°¡¸é¿ª¼º ÃéÀå¿°, ½Å¿ì Á¾±«
IgG4-related kidney disease, Autoimmune pancreatitis, Renal pelvic mass
KMID :
0882420140870060710
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