´Ù±â°üÀ» ħ¹üÇÑ ¸é¿ª±Û·ÎºÒ¸° G4 ºñ¿¬°ü¼º ¼¶À¯°æȼº ´ëµ¿¸ÆÁÖÀ§¿°
Non-IgG4-Related Fibrosclerosing Periaortitis with Multisystemic Involvement
´ëÇѳ»°úÇÐȸÁö 2014³â 86±Ç 6È£ p.749 ~ p.754
ÀÌÁö¿µ(Lee Ji-Young) - ¼º±Õ°ü´ëÇб³ ÀÇ°ú´ëÇÐ »ï¼º¼¿ïº´¿ø ³»°ú
±èÁöÈÆ(Kim Ji-Hoon) - ¼º±Õ°ü´ëÇб³ ÀÇ°ú´ëÇÐ »ï¼º¼¿ïº´¿ø ³»°ú
ÀÌÁöÀ±(Lee Jee-Yun) - ¼º±Õ°ü´ëÇб³ ÀÇ°ú´ëÇÐ »ï¼º¼¿ïº´¿ø ³»°ú
ÀÓ¼ºÈñ(Lim Sung-Hee) - ¼º±Õ°ü´ëÇб³ ÀÇ°ú´ëÇÐ »ï¼º¼¿ïº´¿ø ³»°ú
ÃÖ±âÈ«(Choi Ki-Hong) - ¼º±Õ°ü´ëÇб³ ÀÇ°ú´ëÇÐ »ï¼º¼¿ïº´¿ø ³»°ú
±èÁ¤¼±(Kim Jung-Sun) - ¼º±Õ°ü´ëÇб³ ÀÇ°ú´ëÇÐ »ï¼º¼¿ïº´¿ø º´¸®°ú
±è´ö°æ(Kim Duk-Kyung) - ¼º±Õ°ü´ëÇб³ ÀÇ°ú´ëÇÐ »ï¼º¼¿ïº´¿ø ³»°ú
Abstract
Fibrosclerosing periaortitis is a rare condition that refers to a spectrum of idiopathic diseases characterized by a fibroinflammatory reaction that extends from the adventitia of the aorta into the surrounding structures. It can be present in either IgG4-related or non-IgG4-related fibrosclerosing periaortitis. IgG4-related fibrosclerosing periaortitis could be associated with concomitant multi-organ involvement. However, non-IgG4-related fibrosclerosing periaortitis has rarely been associated with systemic manifestations. Here, we report a 76-year-old female with non-IgG4-related fibrosclerosing periaortitis, who developed pancytopenia, pleural effusion and ascites, which improved after high dose steroid treatment.
Å°¿öµå
Immunoglobulin G, Retroperitoneal fibrosis
KMID :
0882420140860060749
¿ø¹® ¹× ¸µÅ©¾Æ¿ô Á¤º¸
µîÀçÀú³Î Á¤º¸
À¯È¿¼º°á°ú(Recomendation)