Monoclonal Gammopathy of Undetermined Significance°¡ µ¿¹ÝµÈ °­Á÷¼º ôÃß¿° ȯÀÚ¿¡¼­ ¹ß»ýÇÑ AAÇü ¹× ALÇü ½É¾Æ¹Ð·ÎÀ̵åÁõ
Coexistence of AA and AL Cardiac Amyloidosis in a Patient with Ankylosing Spondylitis Accompanying Monoclonal Gammopathy of Undetermined Significance

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±è¿ìÇö(Kim Woo-Hyeon) - °¡Å縯´ëÇб³ ¼­¿ï¼º¸ðº´¿ø ·ù¸¶Æ¼½º³»°ú
±è¼±¾Æ(Kim Seon-A) - °¡Å縯´ëÇб³ ¼­¿ï¼º¸ðº´¿ø ·ù¸¶Æ¼½º³»°ú
À±°æÁø(Yun Kyung-Jin) - °¡Å縯´ëÇб³ ¼­¿ï¼º¸ðº´¿ø ·ù¸¶Æ¼½º³»°ú
³ª¼öÁø(Na Soo-Jin) - °¡Å縯´ëÇб³ ¼­¿ï¼º¸ðº´¿ø ·ù¸¶Æ¼½º³»°ú
ÇöÁöÀÎ(Hyun Ji-In) - °¡Å縯´ëÇб³ ¼­¿ï¼º¸ðº´¿ø ·ù¸¶Æ¼½º³»°ú
Á¤Á¤ÀÓ(Jung Jung-Im) - °¡Å縯´ëÇб³ ¼­¿ï¼º¸ðº´¿ø ¿µ»óÀÇÇаú
°û½Â±â(Kwok Seung-Ki) - °¡Å縯´ëÇб³ ¼­¿ï¼º¸ðº´¿ø ·ù¸¶Æ¼½º³»°ú
¹Ú¼ºÈ¯(Park Sung-Hwan) - °¡Å縯´ëÇб³ ¼­¿ï¼º¸ðº´¿ø ·ù¸¶Æ¼½º³»°ú

Abstract

Amyloidosis is a clinical disorder caused by extracellular deposition of proteinaceous insoluble fibrils in various tis-sues, resulting in organ compromise. Amyloid L (AL) amy-loidosis is the most common type of systemic amyloidosis, which occurs in association with multiple myeloma or monoclonal gammopathy of undetermined significance (MGUS). Secondary amyloid A (AA) amyloidosis is a com-plication of chronic inflammatory conditions, such as rheu-matoid arthritis or ankylosing spondylitis. We report a case of a 49-year-old manwith a 11-year history of anky-losing spondylitis, who was recently diagnosed with MGUS presented with cardiac amyloidosis of both the AA and AL types. We report this case along with a review of relevant literature.

Ű¿öµå

Cardiac amyloidosis, Ankylosing spondylitis Monoclonal gammopathy of undetermined significance
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