A 6-year-old girl with vaginal spotting who was diagnosed with perivascular epithelioid cell neoplasm after vaginoscopic resection
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Á¶ÇöÁ¤(Cho Hyun-Jung) - University of Ulsan College of Medicine Asan Medical Center Department of Obstetrics and Gynecology
À̹̰æ(Lee Mi-Kyung) - University of Ulsan College of Medicine Asan Medical Center Department of Obstetrics and Gynecology
°º´¹®(Kang Byung-Moon) - University of Ulsan College of Medicine Asan Medical Center Department of Obstetrics and Gynecology
±è¼ºÈÆ(Kim Sung-Hoon) - University of Ulsan College of Medicine Asan Medical Center Department of Obstetrics and Gynecology
äÈñµ¿(Chae Hee-Dong) - University of Ulsan College of Medicine Asan Medical Center Department of Obstetrics and Gynecology
±èÁ¤ÈÆ(Kim Chung-Hoon) - University of Ulsan College of Medicine Asan Medical Center Department of Obstetrics and Gynecology
Abstract
Perivascular epithelioid cell neoplasm (PEComa) is a rare tumor with unknown malignant potential. We report a case of a 6-year-old child with history of brain tumor (pineoblastoma), who presented with intermittent vaginal spotting for 6 months. A vaginoscopy revealed a 1.5¡¿1.0-cm mass on the vaginal wall. Pathological examination demonstrated that the tumor was composed of clear cells with organoid patterns, which were immunohistochemically positive for HMB-45 and TFE3, and negative for CK, HNF1-B, SOX10, Melan A, and S-100 protein. These findings were consistent with PEComa arising from the vagina. Regular follow-up with magnetic resonance imaging has shown no signs of recurrence. This case shows that early detection of PEComa and subsequent regular follow-ups are important because of the neoplasm¡¯s unknown malignant potential.
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Perivascular epithelioid cell neoplasms, Resection, Vagina, Vaginoscopy
KMID :
0358420140570050409
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