Treatment of hyperlipidemia associated with Niemann-Pick disease type B by fenofibrate.

Choi, Jin-Ho; Shin, Young-Lim; Kim, Gu-Hwan; Hong, Soo-Jong; Yoo, Han-Wook
European journal of pediatrics
2006Feb ; 165 ( 2 ) :138-9.
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Choi, Jin-Ho -
Shin, Young-Lim -
Kim, Gu-Hwan -
Hong, Soo-Jong -
Yoo, Han-Wook -
ABSTRACT
Lovastatin; Fenofibrate; Autosomal Recessive Disease; Compound Heterozygosity; Acid Sphingomyelinase
MESH
Alanine Transaminase/analysis, Aspartate Aminotransferases/analysis, Child, Preschool, Fenofibrate/*therapeutic use, Humans, Hyperlipidemias/*drug therapy/etiology, Hypolipidemic Agents/*therapeutic use, Male, Niemann-Pick Disease, Type B/*complications
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This study described a NPD type B patient who presented with respiratory symptoms, hepatomegaly, and hyperlipidemia treated with a lipid lowering agent, fenofibrate.
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DOI
10.1007/s00431-005-0009-8
KCDÄÚµå
ICD 03
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